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DeCS
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Descriptor English:
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Neurilemmoma
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Descriptor Spanish:
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Neurilemoma
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Descriptor Portuguese:
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Neurilemoma
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Synonyms English:
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MPNST
Malignant Neurilemmoma
Malignant Neurilemoma
Neurilemoma
Peripheral Nerve Sheath Tumors, Malignant
Schwannoma, Malignant
MPNSTs
Malignant Neurilemmomas
Malignant Neurilemomas
Malignant Schwannoma
Malignant Schwannomas
Neurilemmoma, Malignant
Neurilemmomas
Neurilemmomas, Malignant
Neurilemmosarcomas
Neurilemoma, Malignant
Neurilemomas
Neurilemomas, Malignant
Neurinomas
Plexiform Schwannomatoses
Plexiform Schwannomatosis
Schwannomas
Schwannomas, Malignant
Schwannomatoses, Plexiform
Neurinoma
Schwannoma
Neurilemmosarcoma
Malignant Peripheral Nerve Sheath Tumors
Schwannomatosis, Plexiform
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Tree Number:
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C04.557.465.625.650.595
C04.557.580.600.610.595
C04.557.580.625.650.595
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Definition English:
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A neoplasm that arises from SCHWANN CELLS of the cranial, peripheral, and autonomic nerves. Clinically, these tumors may present as a cranial neuropathy, abdominal or soft tissue mass, intracranial lesion, or with spinal cord compression. Histologically, these tumors are encapsulated, highly vascular, and composed of a homogenous pattern of biphasic fusiform-shaped cells that may have a palisaded appearance. (From DeVita Jr et al., Cancer: Principles and Practice of Oncology, 5th ed, pp964-5) |
Indexing Annotation English:
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benign or malignant; coordinate IM with precoordinated organ/neoplasm term (IM); ameloblastic neurilemmoma goes under ODONTOGENIC TUMORS
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History Note English:
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1999 (1966)
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Allowable Qualifiers English:
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Record Number:
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9635
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Unique Identifier:
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D009442
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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