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DeCS
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Descriptor English:
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Dermatomyositis
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Descriptor Spanish:
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Dermatomiositis
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Descriptor Portuguese:
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Dermatomiosite
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Synonyms English:
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Dermatomyositis, Adult Type
Dermatomyositis, Childhood Type
Dermatopolymyositis
Adult Type Dermatomyositides
Adult Type Dermatomyositis
Childhood Type Dermatomyositides
Childhood Type Dermatomyositis
Dermatomyositides
Dermatomyositides, Adult Type
Dermatomyositides, Childhood Type
Dermatopolymyositides
Polymyositis Dermatomyositis
Polymyositis-Dermatomyositides
Polymyositis-Dermatomyositis
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Tree Number:
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C05.651.594.819.500
C10.668.491.562.575.500
C17.300.250
C17.800.185
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Definition English:
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A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6) |
Indexing Annotation English:
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coord IM with PARANEOPLASTIC SYNDROMES (IM) if pertinent
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Allowable Qualifiers English:
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Record Number:
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3902
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Unique Identifier:
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D003882
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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