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DeCS
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Descriptor English:
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Hyperostosis, Cortical, Congenital
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Descriptor Spanish:
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Hiperostosis Cortical Congénita
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Descriptor Portuguese:
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Hiperostose Cortical Congênita
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Synonyms English:
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Caffey Disease
Congenital Hyperostosis, Cortical
Cortical Congenital Hyperostosis
Familial Caffey's Disease
Familial Infantile Cortical Hyperostosis
Caffey De Toni Silvermann Syndrome
Caffey's Disease, Familial
Congenital Cortical Hyperostoses
Congenital Cortical Hyperostosis
Congenital Hyperostoses, Cortical
Cortical Congenital Hyperostoses
Cortical Hyperostoses, Congenital
Cortical Hyperostoses, Infantile
Cortical Hyperostosis, Infantile
Disease, Caffey
Disease, Familial Caffey's
Familial Caffey Disease
Familial Caffeys Disease
Hyperostoses, Congenital Cortical
Hyperostoses, Cortical Congenital
Hyperostoses, Infantile Cortical
Hyperostosis, Congenital Cortical
Hyperostosis, Cortical Congenital
Hyperostosis, Infantile Cortical
Infantile Cortical Hyperostoses
Syndrome, Caffey-De Toni-Silvermann
Infantile Cortical Hyperostosis
Caffey-De Toni-Silvermann Syndrome
Cortical Hyperostosis, Congenital
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Tree Number:
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C05.116.099.708.479
C05.116.540.400
C16.614.465
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Definition English:
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A disease of young infants characterized by soft tissue swellings over the affected bones, fever, and irritability, and marked by periods of remission and exacerbation. (Dorland, 27th ed) |
Indexing Annotation English:
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cortical refers to cortex of bone; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
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History Note English:
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91; was HYPEROSTOSIS, CORTICAL CONGENITAL 1964-90
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Allowable Qualifiers English:
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Record Number:
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29270
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Unique Identifier:
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D006958
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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