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DeCS
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Descriptor English:
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Paget Disease, Extramammary
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Descriptor Spanish:
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Enfermedad de Paget Extramamaria
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Descriptor Portuguese:
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Doença de Paget Extramamária
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Synonyms English:
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Extra-Mammary Paget Disease
Extra-Mammary Paget's Disease
Extramammary Paget Disease
Extramammary Paget's Disease
Paget Disease, Extra-Mammary
Paget's Disease, Extra-Mammary
Extra Mammary Paget Disease
Extra Mammary Paget's Disease
Extra-Mammary Pagets Disease
Extramammary Pagets Disease
Extramammary, Paget Disease
Paget Disease, Extra Mammary
Paget's Disease, Extra Mammary
Pagets Disease, Extra-Mammary
Pagets Disease, Extramammary
Paget Disease Extramammary
Paget's Disease, Extramammary
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Tree Number:
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C04.557.470.200.025.660
C04.557.470.615.660
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Definition English:
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A rare cutaneous neoplasm that occurs in the elderly. It develops more frequently in women and predominantly involves apocrine gland-bearing areas, especially the vulva, scrotum, and perianal areas. The lesions develop as erythematous scaly patches that progress to crusted, pruritic, erythematous plaques. The clinical differential diagnosis includes squamous cell carcinoma in situ and superficial fungal infection. It is generally thought to be an adenocarcinoma of the epidermis, from which it extends into the contiguous epithelium of hair follicles and eccrine sweat ducts. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1478) |
Indexing Annotation English:
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neoplastic; /blood supply /chem /second /secret /ultrastruct permitted; coord IM with precoord organ/neopl term (IM)
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History Note English:
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2010(1963)
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Allowable Qualifiers English:
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Record Number:
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31760
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Unique Identifier:
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D010145
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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