Search on:
ERDHEIM-CHESTER DISEASE
Descriptors Found:
1
Displaying:
1 .. 1
1 / 1
DeCS
Descriptor
English
:
Erdheim-Chester Disease
Descriptor
Spanish
:
Enfermedad de Erdheim-Chester
Descriptor
Portuguese
:
Doença de Erdheim-Chester
Synonyms
English
:
Erdheim Chester Disease
Lipid Granulomatosis
Granulomatosis, Lipid
Tree Number:
C15.604.250.410.224
Definition
English
:
A rare form of non-Langerhans-cell
histiocytosis
(
HISTIOCYTOSIS
, NON-LANGERHANS-CELL) with onset in
middle age
. The systemic
disease
is characterized by infiltration of lipid-laden
macrophages
, multinucleated
giant cells
, an inflammatory infiltrate of
lymphocytes
and
histiocytes
in the
bone marrow
, and a generalized
sclerosis
of the long bones.
History Note
English
:
2003
Allowable Qualifiers
English
:
BL
blood
CF
cerebrospinal fluid
CI
chemically induced
CL
classification
CO
complications
CN
congenital
DI
diagnosis
DG
diagnostic imaging
DH
diet therapy
DT
drug therapy
EC
economics
EM
embryology
EN
enzymology
EP
epidemiology
EH
ethnology
ET
etiology
GE
genetics
HI
history
IM
immunology
ME
metabolism
MI
microbiology
MO
mortality
NU
nursing
PS
parasitology
PA
pathology
PP
physiopathology
PC
prevention & control
PX
psychology
RT
radiotherapy
RH
rehabilitation
SU
surgery
TH
therapy
UR
urine
VE
veterinary
VI
virology
Record Number:
37288
Unique Identifier:
D031249
Occurrence in VHL
:
Similar:
DeCS
CID-10
SciELO
LILACS
LIS