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DeCS
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Descriptor English:
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Multiple Endocrine Neoplasia
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Descriptor Spanish:
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Neoplasia Endocrina Múltiple
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Descriptor Portuguese:
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Neoplasia Endócrina Múltipla
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Synonyms English:
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Adenomatosis, Multiple Endocrine
Familial Endocrine Adenomatosis
Multiple Endocrine Adenomatosis
Multiple Endocrine Adenopathy
Multiple Endocrine Neoplasia Syndromes
Multiple Endocrine Neoplasms
Adenomatoses, Familial Endocrine
Adenomatoses, Multiple Endocrine
Adenopathies, Multiple Endocrine
Adenopathy, Multiple Endocrine
Endocrine Adenomatoses, Familial
Endocrine Adenomatoses, Multiple
Endocrine Adenomatosis, Familial
Endocrine Adenomatosis, Multiple
Endocrine Adenopathies, Multiple
Endocrine Adenopathy, Multiple
Endocrine Neoplasms, Multiple
Familial Endocrine Adenomatoses
Multiple Endocrine Adenomatoses
Multiple Endocrine Adenopathies
Adenomatosis, Familial Endocrine
Endocrine Neoplasia, Multiple
Neoplasia, Multiple Endocrine
Neoplasms, Multiple Endocrine
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Tree Number:
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C04.588.322.400
C04.651.600
C04.700.630
C16.320.700.630
C19.344.400
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Definition English:
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A group of autosomal dominant diseases characterized by the combined occurrence of tumors involving two or more ENDOCRINE GLANDS that secrete PEPTIDE HORMONES or AMINES. These neoplasias are often benign but can be malignant. They are classified by the endocrine glands involved and the degree of aggressiveness. The two major forms are MEN1 and MEN2 with gene mutations on CHROMOSOME 11 and CHROMOSOME 10, respectively. |
Indexing Annotation English:
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general or unspecified; prefer specifics; coordinate IM with specific endocrine/neoplasm pre-coordinates (IM) + specific histological type (IM) if pertinent; DF MULTIPLE ENDOCRINE NEOPL
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History Note English:
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95; was NEOPLASMS, MULTIPLE ENDOCRINE 1983-94; was ADENOMATOSIS, FAMILIAL ENDOCRINE 1965-82 (Prov 1964)
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Allowable Qualifiers English:
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Record Number:
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22577
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Unique Identifier:
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D009377
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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